Abstract

YEPEZ, Cristian Vinicio Bravo et al. Management of Klippel-Trenaunay Syndrome: case report. Vive Rev. Salud [online]. 2023, vol.6, n.16, pp.154-161.  Epub Feb 14, 2023. ISSN 2664-3243.  https://doi.org/10.33996/revistavive.v6i16.214.

Klippel-Trenaunay syndrome is a complex vascular malformation with an incidence of 2 to 3 cases per 100,000 live births. Clinically, it presents a classic triad: port-wine stains, varicose veins of atypical location and bone and soft tissue hypertrophy. We present the case of a 33-year-old female patient, with no pathologic or surgical history of importance, who comes to the clinic for an increase in volume of the right extremity, ipsilateral violaceous spot, in addition to pain and paresthesia. Physical examination revealed longitudinal enlargement of the right lower limb, hyperpigmented nevus on the lateral aspect of the right leg and thigh extending to the ipsilateral buttock and atypical varicose veins. Venous Doppler ultrasound with linear transducer reported incompetence of the greater saphenous vein and supragenicular perforators. Surgical management was performed by saphenectomy, deformity correction and referral to dermatology for laser therapy for hyperpigmented nevus. The patient showed favorable clinical-surgical evolution with remission of the symptomatology that motivated her consultation.

Keywords : Klippel-Trenaunay Syndrome; Varicose veins; doppler Ultrasound.

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